c.4882C>T (p.Gln1628X)
Variant ID | Exon |
46 | Exon 37 |
RNA effect | EPP | Control frequency | Controls origin |
RNA stability | 3 | 0/94 | Central Europe, Middle East, East Asia and US |
The reading frame is interrupted by a premature STOP codon.
The mRNA produced might be targeted for nonsense mediated decay (NMD).
Patient information | Allele 1 | Allele 2 | |||||||||||||||
Patient ID | Family ID | Gender | Age | Origin | Disease | Segregation | Parental consanguinity | Consanguinity degree | Exon/intron | Nucleotide nomencl. | Protein nomencl. | Detection method | Exon/intron | Nucleotide nomencl. | Protein nomencl. | Detection method | Reference |
247 | 2 y | France | LCA | unknown | unknown | Exon 37 | c.4882C>T | p.Gln1628X | Direct sequencing (Sanger) | Intron 26 | c.2991+1655A>G | p.Cys998X | Direct sequencing (Sanger) | Perrault (2007) | |||
MTI333a | MTI333 | male | 3 y | United States Of America | JS + retina | yes | no | Exon 37 | 4882C>T | Q1628X | DHPLC | Exon 41 | 5610delCAAA | K1870fsX1872 | DHPLC | Brancati (2007) | |
MTI333b | MTI333 | female | 12 y | United States Of America | CORS | yes | no | Exon 37 | 4882C>T | Q1628X | DHPLC | Exon 41 | 5610delCAAA | K1870fsX1872 | DHPLC | Brancati (2007) | |
COR084 | female | 6 y | Russian Federation | CORS | unknown | no | Exon 37 | 4882C>T | Q1628X | DHPLC | Exon 43 | 5941G>T | E1981X | DHPLC | Brancati (2007) | ||
P3 | male | 14 y | LCA | unknown | unknown | c.4882C>T | p.Q1628X | Intron 26 | c.2991+1655A>G | Splice defect | Cideciyan (2007) | ||||||
A989 II-1 | A989 | Switzerland | CORS | unknown | no | Exon 38 | C4882T | Q1628X | DHPLC | Exon 44 | G5941T | E1981X | DHPLC | Helou (2007) |