Overview
Show graphical representation of the mutations.
Variant ID | Variation type | Exon/intron | Nucleotide nomencl. | Base change type | Protein nomencl. | Protein change type | Number of probands | dbSNP ID | OMIM ID | Swiss-Prot ID |
227 | mutation | Exon 7 | c.451C>T | base substitution | p.Arg151X | in-frame deletion | 0 | |||
34 | mutation | Exon 2 - CDS | c.2T>A | base substitution | p.Met1? | unknown | 1 | |||
91 | mutation | Exon 2 - CDS | c.1A>G | base substitution | p.Met1? | unknown | 1 | |||
5 | mutation | Exon 2 - CDS | c.21G>T | base substitution | p.Trp7Cys | missense (aminoacid sub) | 2 | rs62635288 | 610142.0003 | VAR_028356 |
53 | mutation | Intron 2 | c.103-13_103-18del | base(s) deletion | p.? | unknown | 2 | |||
93 | mutation | Exon 3 | c.164_167del | base(s) deletion | p.Thr55SerfsX3 | truncating deletion | 1 | |||
22 | mutation | Intron 3 | c.180+1G>T | base substitution | p.? | unknown | 1 | |||
82 | mutation | Intron 3 | c.180+2T>A | base substitution | p.? | unknown | 1 | 610142.0009 | ||
21 | mutation | Exon 5 | c.265dup | duplication | p.Thr89AsnfsX2 | truncating deletion | 1 | rs62642052 | ||
78 | mutation | Exon 5 | c.287del | base(s) deletion | p.Asn96MetfsX29 | truncating deletion | 1 | |||
115 | polymorphism | Intron 5 | c.297+36A>G | base substitution | p.? | unknown | 1 | rs45468703 | ||
146 | mutation | Exon 6 | c.322C>T | base substitution | p.Arg108X | nonsense (stop codon) | 1 | |||
83 | mutation | Exon 6 | c.381_382delinsT | complex | p.Lys127AsnfsX36 | truncating deletion | 1 | |||
51 | mutation | Exon 6 | c.384_387del | base(s) deletion | p.Asp128GlufsX34 | truncating deletion | 3 | 610142.0008 | ||
160 | mutation | Exon 6 | c.384_385del | base(s) deletion | p.Asp128GlufsX17 | truncating deletion | 1 | |||
162 | mutation | Exon 6 | c.437del | base(s) deletion | p.Glu146GlyfsX17 | truncating deletion | 1 | |||
98 | mutation | Exon 9 | c.566C>G | base substitution | p.Ser189X | nonsense (stop codon) | 1 | |||
80 | mutation | Exon 9 | c.613C>T | base substitution | p.Arg205X | nonsense (stop codon) | 1 | 610142.0010 | ||
20 | mutation | Exon 10 | c.679_680del | base(s) deletion | p.Glu227SerfsX2 | truncating deletion | 1 | rs62640578 | ||
117 | polymorphism | Exon 10 | c.829G>C | base substitution | p.Glu277Gln | missense (aminoacid sub) | 1 | rs45502896 | ||
118 | unclassified variant | Exon 11 | c.930A>G | base substitution | p.= | no effect | 1 | |||
90 | mutation | Intron 12 | c.1066-1G>A | base substitution | p.? | unknown | 2 | |||
176 | mutation | Intron 13 | c.1189+1G>A | base substitution | p.? | unknown | 1 | |||
32 | mutation | Exon 14 | c.1219_1220del | base(s) deletion | p.Met407GlufsX14 | truncating deletion | 4 | |||
79 | mutation | Exon 14 | c.1260_1264del | base(s) deletion | p.Lys421GlyfsX2 | truncating deletion | 2 | 610142.0011 | ||
75 | mutation | Exon 15 | c.1361del | base(s) deletion | p.Gly454GlufsX5 | truncating deletion | 1 | |||
92 | mutation | Exon 15 | c.1419_1423del | base(s) deletion | p.Ile474ArgfsX5 | truncating deletion | 1 | |||
23 | mutation | Exon 16 | c.1550del | base(s) deletion | p.Leu517X | nonsense (stop codon) | 1 | rs62640579 | ||
33 | mutation | Exon 16 | c.1593C>A | base substitution | p.Tyr531X | nonsense (stop codon) | 1 | |||
73 | mutation | Exon 17 | c.1645C>T | base substitution | p.Arg549X | nonsense (stop codon) | 1 | |||
54 | mutation | Exon 17 | c.1666del | base(s) deletion | p.Ile556PhefsX17 | truncating deletion | 1 | |||
57 | mutation | Exon 17 | c.1682_1683del | base(s) deletion | p.Gln561ArgfsX14 | truncating deletion | 1 | |||
39 | mutation | Exon 17 | c.1709C>G | base substitution | p.Ser570X | nonsense (stop codon) | 1 | |||
42 | mutation | Intron 17 | c.1711+5A>G | base substitution | p.? | unknown | 1 | |||
189 | mutation | Exon 18 | c.1824G>A | base substitution | p.= | no effect | 1 | |||
28 | mutation | Exon 19 | c.1859_1862del | base(s) deletion | p.Arg621IlefsX2 | truncating deletion | 2 | |||
84 | mutation | Exon 19 | c.1860_1861del | base(s) deletion | p.Asp622PhefsX5 | truncating deletion | 1 | |||
206 | mutation | Intron 19 | c.1910-2A>C | base substitution | p.? | unknown | 1 | |||
43 | mutation | Exon 20 | c.1936C>T | base substitution | p.Gln646X | nonsense (stop codon) | 1 | |||
62 | mutation | Exon 20 | c.1985A>T | base substitution | p.Gln662Leu | missense (aminoacid sub) | 1 | |||
89 | mutation | Exon 20 | c.1984C>T | base substitution | p.Gln662X | nonsense (stop codon) | 1 | |||
96 | unclassified variant | Exon 20 | c.1991A>G | base substitution | p.Asp664Gly | missense (aminoacid sub) | 2 | |||
31 | mutation | Exon 20 | c.1992del | base(s) deletion | p.Pro665LeufsX10 | truncating deletion | 1 | |||
120 | polymorphism | Intron 20 | c.2052+30del | base(s) deletion | p.? | unknown | 1 | rs11358611 | ||
121 | polymorphism | Exon 21 | c.2055T>C | base substitution | p.= | no effect | 1 | |||
17 | mutation | Exon 21 | c.2118_2122dup | duplication | p.Thr709SerfsX9 | truncating deletion | 1 | rs62640580 | ||
122 | polymorphism | Intron 21 | c.2217+45T>C | base substitution | p.? | unknown | 1 | rs45461003 | ||
7 | mutation | Intron 21 | c.2218-4_2222del | base(s) deletion | p.? | unknown | 1 | 610142.0004 | ||
101 | mutation | Exon 22 | c.2218-15_2220del | base(s) deletion | p.? | unknown | 1 | |||
178 | mutation | Intron 21 | c.2218-2A>C | base substitution | p.? | unknown | 1 | |||
16 | mutation | Exon 22 | c.2249T>G | base substitution | p.Leu750X | nonsense (stop codon) | 2 | 610142.0006 | ||
71 | mutation | Exon 22 | c.2251C>T | base substitution | p.Arg751X | nonsense (stop codon) | 1 | |||
123 | polymorphism | Exon 22 | c.2268G>A | base substitution | p.= | no effect | 1 | rs2468255 | ||
124 | unclassified variant | Exon 22 | c.2343T>C | base substitution | p.= | no effect | 1 | |||
125 | polymorphism | Exon 24 | c.2512A>G | base substitution | p.Lys838Glu | missense (aminoacid sub) | 1 | rs11104738 | ||
148 | mutation | Exon 25 | c.2695C>T | base substitution | p.Gln899X | nonsense (stop codon) | 1 | |||
126 | unclassified variant | Exon 25 | c.2717T>G | base substitution | p.Leu906Trp | missense (aminoacid sub) | 1 | rs7970228 | ||
85 | mutation | Exon 26 | c.2906dup | duplication | p.Tyr969X | nonsense (stop codon) | 1 | |||
15 | mutation | Intron 26 | c.2991+1655A>G | base substitution | p.Cys998X; wild-type | nonsense (stop codon) | 83 | 610142.0005 | ||
87 | mutation | Exon 27 | c.3043G>T | base substitution | p.Glu1015X | nonsense (stop codon) | 1 | |||
88 | mutation | Intron 27 | c.3104-1G>A | base substitution | p.? | unknown | 1 | |||
94 | mutation | Intron 27 | c.3104-2A>G | base substitution | p.? | unknown | 1 | |||
4 | mutation | Exon 28 | c.3176del | base(s) deletion | p.Ile1059LysfsX6 | truncating deletion | 1 | |||
11 | mutation | Exon 28 | c.3175dup | duplication | p.Ile1059AsnfsX11 | truncating deletion | 3 | rs62640570 | ||
81 | mutation | Exon 28 | c.3175del | base(s) deletion | p.Ile1059X | nonsense (stop codon) | 1 | |||
48 | mutation | Exon 28 | c.3292G>T | base substitution | p.Glu1098X | nonsense (stop codon) | 2 | |||
76 | mutation | Intron 28 | c.3310-1G>C | base substitution | p.? | unknown | 1 | |||
180 | mutation | Intron 28 | c.3310-1_3310delinsAA | complex | p.? | unknown | 3 | |||
166 | mutation | Exon 29 | c.3422dup | duplication | p.Leu1141PhefsX5 | truncating deletion | 1 | |||
86 | mutation | Exon 31 | c.3793C>T | base substitution | p.Gln1265X | nonsense (stop codon) | 2 | |||
60 | mutation | Exon 31 | c.3811C>T | base substitution | p.Arg1271X | nonsense (stop codon) | 3 | |||
19 | mutation | Exon 31 | c.3814C>T | base substitution | p.Arg1272X | nonsense (stop codon) | 2 | rs62640581 | ||
47 | mutation | Exon 31 | c.3922C>T | base substitution | p.Gln1308X | nonsense (stop codon) | 1 | |||
168 | mutation | Exon 31 | c.4001del | base(s) deletion | p.Thr1334IlefsX2 | truncating deletion | 1 | |||
50 | mutation | Exon 31 | c.4028del | base(s) deletion | p.Lys1343ArgfsX2 | truncating deletion | 1 | |||
24 | mutation | Exon 32 | c.4115_4116del | base(s) deletion | p.Ile1372LysfsX5 | truncating deletion | 2 | rs62640582 | ||
140 | mutation | Exon 32 | c.4114_4115del | base(s) deletion | p.Ile1372LysfsX5 | truncating deletion | 1 | |||
74 | mutation | Intron 32 | c.4195-1G>A | base substitution | p.? | unknown | 1 | |||
59 | mutation | Exon 34 | c.4393C>T | base substitution | p.Arg1465X | nonsense (stop codon) | 6 | |||
6 | mutation | Exon 35 | c.4656del | base(s) deletion | p.Glu1553LysfsX4 | truncating deletion | 1 | rs62640572 | 610142.0002 | |
41 | mutation | Exon 35 | c.4661_4663del | base(s) deletion | p.Glu1554del | in-frame deletion | 1 | |||
188 | unclassified variant | Exon 35 | c.4696G>C | base substitution | p.Ala1566Pro | missense (aminoacid sub) | 1 | |||
127 | polymorphism | Intron 35 | c.4704+46del | base(s) deletion | p.? | unknown | 1 | rs11356711 | ||
35 | mutation | Exon 36 | c.4723A>T | base substitution | p.Lys1575X | nonsense (stop codon) | 16 | 610142.0007 | ||
1 | mutation | Exon 36 | c.4732G>T | base substitution | p.Glu1578X | nonsense (stop codon) | 1 | rs62640573 | ||
8 | mutation | Exon 36 | c.4771C>T | base substitution | p.Gln1591X | nonsense (stop codon) | 1 | rs62640574 | ||
64 | mutation | Exon 36 | c.4791_4794del | base(s) deletion | p.Lys1598SerfsX8 | truncating deletion | 1 | |||
128 | unclassified variant | Exon 36 | c.4806G>A | base substitution | p.= | no effect | 1 | |||
46 | mutation | Exon 37 | c.4882C>T | base substitution | p.Gln1628X | nonsense (stop codon) | 5 | |||
25 | mutation | Exon 37 | c.4966G>T | base substitution | p.Glu1656X | nonsense (stop codon) | 1 | rs62638179 | ||
49 | mutation | Exon 37 | c.4962_4963del | base(s) deletion | p.Glu1656AsnfsX3 | truncating deletion | 2 | |||
52 | mutation | Exon 37 | c.4965_4966del | base(s) deletion | p.Glu1656AsnfsX3 | truncating deletion | 1 | |||
99 | mutation | Exon 38 | c.5046del | base(s) deletion | p.Val1683X | nonsense (stop codon) | 1 | |||
190 | unclassified variant | Exon 38 | c.5081T>C | base substitution | p.Leu1694Pro | missense (aminoacid sub) | 1 | |||
30 | mutation | Exon 38 | c.5163del | base(s) deletion | p.Thr1722GlnfsX2 | truncating deletion | 5 | |||
29 | mutation | Intron 38 | c.5226+1G>A | base substitution | p.? | unknown | 1 | |||
45 | mutation | Exon 39 | c.5256_5257del | base(s) deletion | p.Ala1753ArgfsX7 | truncating deletion | 1 | |||
158 | mutation | Exon 39 | c.5344C>T | base substitution | p.Arg1782X | nonsense (stop codon) | 1 | |||
65 | mutation | Exon 40 | c.5434_5435del | base(s) deletion | p.Glu1812LysfsX5 | truncating deletion | 1 | |||
69 | mutation | Exon 40 | c.5493del | base(s) deletion | p.Ala1832ProfsX19 | truncating deletion | 4 | 610142.0012 | ||
12 | mutation | Exon 40 | c.5515_5518del | base(s) deletion | p.Glu1839LysfsX11 | truncating deletion | 1 | rs62640576 | ||
172 | mutation | Exon 40 | c.5519_5537del | base(s) deletion | p.Lys1840ArgfsX5 | truncating deletion | 1 | |||
27 | mutation | Intron 40 | c.5587-1G>C | base substitution | p.? | unknown | 5 | |||
56 | mutation | Exon 41 | c.5611_5614del | base(s) deletion | p.Gln1871ValfsX2 | truncating deletion | 1 | |||
13 | mutation | Exon 41 | c.5649dup | duplication | p.Leu1884ThrfsX23 | truncating deletion | 4 | rs62642051 | ||
2 | mutation | Exon 41 | c.5668G>T | base substitution | p.Gly1890X | nonsense (stop codon) | 11 | 610142.0001 | ||
36 | mutation | Exon 41 | base substitution | p.Glu1903X | nonsense (stop codon) | 1 | 610142.0013 | |||
129 | polymorphism | Intron 41 | c.5709+25A>C | base substitution | p.? | unknown | 1 | rs17015438 | ||
130 | polymorphism | Intron 41 | c.5709+45G>C | base substitution | p.? | unknown | 1 | rs45477793 | ||
66 | mutation | Exon 42 | c.5722G>T | base substitution | p.Glu1908X | nonsense (stop codon) | 1 | |||
61 | mutation | Exon 42 | c.5734del | base(s) deletion | p.Trp1912GlyfsX11 | truncating deletion | 2 | |||
100 | mutation | Exon 42 | c.5776C>T | base substitution | p.Arg1926X | nonsense (stop codon) | 1 | |||
26 | mutation | Exon 42 | c.5813_5817del | base(s) deletion | p.Thr1938AsnfsX16 | truncating deletion | 1 | rs62638180 | ||
3 | mutation | Exon 42 | c.5824C>T | base substitution | p.Gln1942X | nonsense (stop codon) | 1 | |||
40 | mutation | Exon 42 | c.5850del | base(s) deletion | p.Phe1950LeufsX15 | truncating deletion | 5 | |||
18 | mutation | Exon 43 | c.5866G>T | base substitution | p.Glu1956X | nonsense (stop codon) | 1 | |||
174 | mutation | Exon 43 | c.5865_5867delinsGG | complex | p.Glu1956GlyfsX9 | truncating deletion | 1 | |||
95 | mutation | Exon 43 | c.5932C>T | base substitution | p.Arg1978X | nonsense (stop codon) | 1 | |||
58 | mutation | Exon 43 | c.5941G>T | base substitution | p.Glu1981X | nonsense (stop codon) | 2 | |||
55 | mutation | Exon 44 | c.6031C>T | base substitution | p.Arg2011X | nonsense (stop codon) | 1 | |||
67 | mutation | Exon 44 | c.6072C>A | base substitution | p.Tyr2024X | nonsense (stop codon) | 1 | |||
77 | mutation | Intron 45 | c.6271-8T>G | base substitution | p.? | unknown | 1 | |||
63 | mutation | Exon 46 | c.6277del | base(s) deletion | p.Val2093SerfsX4 | truncating deletion | 1 | |||
14 | mutation | Exon 46 | c.6331C>T | base substitution | p.Gln2111X | nonsense (stop codon) | 1 | rs62640577 | ||
131 | polymorphism | Intron 47 | c.6522+12dup | duplication | p.? | unknown | 1 | rs11405846 | ||
44 | mutation | Exon 48 | c.6604del | base(s) deletion | p.Ile2202LeufsX24 | truncating deletion | 2 | |||
132 | unclassified variant | Exon 49 | c.6684T>G | base substitution | p.Asn2228Lys | missense (aminoacid sub) | 1 | |||
72 | mutation | Exon 50 | c.6869del | base(s) deletion | p.Asn2290IlefsX11 | truncating deletion | 2 | |||
70 | mutation | Exon 50 | c.6870del | base(s) deletion | p.Gln2291LysfsX10 | truncating deletion | 1 | |||
133 | polymorphism | Intron 51 | c.7035-38C>G | base substitution | p.? | unknown | 1 | rs45477492 | ||
134 | polymorphism | Intron 53 | c.7210-22T>C | base substitution | p.? | unknown | 1 | rs45613639 | ||
97 | unclassified variant | Exon 54 - CDS | c.7311_7313del | base(s) deletion | p.Lys2437del | in-frame deletion | 1 | |||
68 | mutation | Exon 54 - CDS | c.7318_7321dup | duplication | p.Leu2441SerfsX16 | truncating deletion | 1 | |||
10 | mutation | Exon 54 - CDS | c.7341dup | duplication | p.Leu2448ThrfsX8 | truncating deletion | 2 | |||
200 | mutation | Exon 54 - CDS | c.7366_7369del | base(s) deletion | p.Thr2457AlafsX27 | truncating deletion | 1 |